A family with pachyonychia congenita affecting the nails only
- 1 November 1994
- journal article
- case report
- Published by Oxford University Press (OUP) in Clinical and Experimental Dermatology
- Vol. 19 (6) , 521-522
- https://doi.org/10.1111/j.1365-2230.1994.tb01263.x
Abstract
A family with pachyonychia congenita in which affected individuals showed nail involvement only is described. Pachyonychia congenita is a rare hereditary disorder inherited in an autosomal dominant manner. Various classifications of pachyonychia congenita have been suggested but none indicates nail involvement as a solitary finding.Keywords
This publication has 2 references indexed in Scilit:
- Pachyonychia Congenita: A Clinical Study of 12 Cases and Review of the LiteraturePediatric Dermatology, 1990
- Pachyonychia congenitaJournal of the American Academy of Dermatology, 1988