Accumulation of glycogen in sural nerve axons in adult‐onset type III glycogenosis

Abstract
A 42‐year‐old man with adult‐onset type III glycogenosis (Cori's disease) developed a gradually progressive polyneuropathy with markedly reduced activity of muscle amylo‐1,6‐glucosidase and glycogen accumulation within all elements of biopsied sural nerve, including axons, as shown by ultrastructural assessment.

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