Epidermolysis bullosa hereditaria letalis.
- 1 January 1977
- journal article
- research article
- Published by Oxford University Press (OUP) in British Journal of Dermatology
- Vol. 96 (1) , 51-58
- https://doi.org/10.1111/j.1365-2133.1977.tb05185.x
Abstract
A patient [an infant] with epidermolysis bullosa hereditaria letalis had the characteristic EM lesions not only in the skin, but also in the gastrointestinal, genito-urinary and respiratory tracts. Administration of dexamethasone to this patient resulted in a significant decrease in the blistering. Although the patient died, long term survival in this disease is not rare. Staining tissue specimens from patients with epidermolysis bullosa with fluorescein-labeled bullous pemphigoid antibody is a reliable method for differentiating between junctional and dystrophic disease.This publication has 7 references indexed in Scilit:
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