Bone marrow transplantation does not correct the hyper IgE syndrome
- 1 June 2000
- journal article
- case report
- Published by Springer Nature in Bone Marrow Transplantation
- Vol. 25 (12) , 1303-1305
- https://doi.org/10.1038/sj.bmt.1702446
Abstract
Congenital immunodeficiency in hyper IgE syndrome is characterised by a markedly raised IgE level, recurrent staphylococcal skin infection and pneumatoceles. Standard treatments include anti-staphylococcal antibiotics. We report a severely affected patient in whom successful bone marrow transplantation was followed by reappearance of the immunodeficiency. We conclude that bone marrow transplantation does not cure the immunological features of the hyper IgE syndrome. Bone Marrow Transplantation (2000) 25, 1303-1305.Keywords
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