Chronic suppurative lung disease in sisters mimicking cystic fibrosis
Open Access
- 1 July 1974
- journal article
- research article
- Published by BMJ in Archives of Disease in Childhood
- Vol. 49 (7) , 520-524
- https://doi.org/10.1136/adc.49.7.520
Abstract
Two sisters are described with fatal chronic obstructive lung disease of unknown origin. The lung condition was clinically and histologically indistinguishable from cystic fibrosis and the salivary glands showed pathological changes expected in cystic fibrosis. Neither child had abnormal sweat electrolytes, they had no bowel symptoms, and the pancreas was normal at necropsy.Keywords
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