Chronic inflammatory demyelinating polyneuropathy of infancy: A corticosteroid‐responsive disorder
- 1 July 1986
- journal article
- research article
- Published by Wiley in Annals of Neurology
- Vol. 20 (1) , 76-81
- https://doi.org/10.1002/ana.410200113
Abstract
We present the clinical, electrophysiological, and histopathological findings in 6 children with early‐onset chronic inflammatory demyelinating neuropathy. The clinical features initially suggested a genetically determined disorder in each patient. Sural nerve biopsy showed changes of chronic demyelination with multifocal endoneurial edema and mononuclear cellular infiltrates. All children improved with corticosteroid therapy.This publication has 16 references indexed in Scilit:
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