Yeast and Human Frataxin Are Processed to Mature Form in Two Sequential Steps by the Mitochondrial Processing Peptidase

This publication has 32 references indexed in Scilit:

• Aconitase and mitochondrial iron–sulphur protein deficiency in Friedreich ataxia
  Nature Genetics, 1997
• Respiratory deficiency due to loss of mitochondrial DNA in yeast lacking the frataxin homologue
  Nature Genetics, 1997
• Studies of human, mouse and yeast homologues indicate a mitochondrial function for frataxin
  Nature Genetics, 1997
• Regulation of Mitochondrial Iron Accumulation by Yfh1p, a Putative Homolog of Frataxin
  Science, 1997
• PROTEIN IMPORT INTO MITOCHONDRIA
  Annual Review of Biochemistry, 1997
• Prediction and Identification of New Natural Substrates of the Yeast Mitochondrial Intermediate Peptidase
  Published by Elsevier ,1995
• Mdj1p, a novel chaperone of the DnaJ family, is involved in mitochondrial biogenesis and protein folding
  Cell, 1994
• Cleavage of precursors by the mitochondrial processing peptidase requires a compatible mature protein or an intermediate octapeptide.
  The Journal of cell biology, 1991
• The mitochondrial chaperonin hsp60 is required for its own assembly
  Nature, 1990
• Mitochondrial protein import: Identification of processing peptidase and of PEP, a processing enhancing protein
  Cell, 1988