Intestinal neurofibromatosis with malignant degeneration

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Abstract
Or was suspected before operation, but the sarcomatous changes came as a surprise. Review of the literature reveals that these tumors associated with von Reckling-hausen's disease are not as rare as is generally thought. We believe, like others, that in all cases of von Recklinghausen's disease x-ray studies should be made of the chest, the gastro-intestinal tract and the large bowel to determine if there are other evidences of neurofibromatosis. When intestinal neurofibromatosis is diagnosed, it should be followed promptly by operation even if there are no clinical symptoms. Malignant degeneration may occur prior to operation, as was true in our case, and despite negative x-ray findings, when there are definite clinical symptoms an operation should be performed. © The ASCRS 1960...