Abnormal Intradermal Histamine Reaction in the Syndrome of Pheochromocytoma, Medullary Carcinoma of the Thyroid Gland and Multiple Mucosal Neuromas

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Abstract
A RECENT review1 has compiled 17 cases of a rare syndrome consisting of pheochromocytonia, medullary carcinoma of the thyroid gland with elevated calcitonin blood levels, multiple mucosal neuromas or neurofibromas (or both), a characteristic facies, a Marfanoid habitus with arachnodactyly, pes cavus, scoliosis and peetus carinatum, decayed teeth with poor enamel, absent facial and axillary hair, visible corneal nerves and thickened eyelids. These findings are not necessarily present in each patient. The patient described below demonstrates all the above findings and, in addition, decreased tear function and an ectopic lacrimal punctum. A particularly interesting feature was an absent flare response after . . .