Abstract
A Caucasian girl with an unusual dermatosis, similar to cutis marmorata telangiectatica congenita of Van Lohuizen is presented. Four of the five main features (congenital phlebectasia, cutis marmorata, superficial ulcerations, and steady improvement) were present. Lacking was spider nevus-like telangiectasias. Recognition is of value as the prognosis is favorable.