Primary pulmonary lymphangiectasis in a premature infant: Resolution following intensive care
- 3 April 2003
- journal article
- case report
- Published by Wiley in Pediatric Pulmonology
- Vol. 35 (5) , 405-406
- https://doi.org/10.1002/ppul.10241
Abstract
Primary pulmonary lymphangiectasis is a rare disease, often described as fatal within the neonatal period. We report on an infant who developed severe bilateral chylous pleural effusions with computed tomography (CT) features of pulmonary lymphangiectasis. She recovered spontaneously with supportive treatment only. We discuss aspects of her intensive care which might have contributed to the good outcome, and conclude that modern intensive care may allow spontaneous recovery in conditions described in the literature as having a very poor outcome. Pediatr Pulmonol. 2003; 35:405–406.Keywords
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