Dietary carnitine supplements slow disease progression in a putative mouse model for hereditary ceroid-lipofuscinosis
- 1 October 1997
- journal article
- research article
- Published by Wiley in Journal of Neuroscience Research
- Vol. 50 (1) , 123-132
- https://doi.org/10.1002/(sici)1097-4547(19971001)50:1<123::aid-jnr13>3.0.co;2-c
Abstract
No abstract availableKeywords
This publication has 38 references indexed in Scilit:
- Effect of intravenous L-carnitine on carnitine homeostasis and fuel metabolism during exercise in humansClinical Pharmacology & Therapeutics, 1994
- Motor neuron degeneration of mice is a model of neuronal ceroid lipofuscinosis (Batten's disease)Annals of Neurology, 1993
- Effect of carnitine feeding on the levels of heart and skeletal muscle carnitine of elderly miceFEBS Letters, 1993
- Neuronal ceroid-lipofuscinoses: The current statusBrain & Development, 1992
- Effects of supplementary levels of L-carnitine on blood and urinary carnitines and on the portal-systemic blood-ethanol concentrations in the ratThe Journal of Nutritional Biochemistry, 1991
- CARNITINEAnnual Review of Biochemistry, 1988
- Reconsideration of the classification of the neuronal ceroid-lipofuscinosesAmerican Journal of Medical Genetics, 1988
- Clinical classification of neuronal ceroid-lipofuscinosis subtypesAmerican Journal of Medical Genetics, 1988
- Morphological studies in canine (Dalmatian) neuronal ceroid-lipofuscinosisAmerican Journal of Medical Genetics, 1988
- Carnitine--metabolism and functionsPhysiological Reviews, 1983