Normal dolichol concentration in urine sediments from four patients with neuronal ceroid lipofuscinosis (Batten's disease)
- 24 April 1986
- journal article
- research article
- Published by Wiley in Journal of Inherited Metabolic Disease
- Vol. 10 (1) , 28-32
- https://doi.org/10.1007/bf01799485
Abstract
The dolichol contents of urine sediments from a patient with infantile (Santavuori), a patient with late infantile (Jansky-Bielschowsky) and two patients with juvenile (Spielmeyer-Vogt) neuronal ceroid lipofuscinosis (Batten's disease) were not elevated when compared to those from healthy controls.Keywords
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