Uptake and intracellular degradation of fluorescent sphingomyelin by fibroblasts from normal individuals and a patient with Niemann-Pick disease
- 1 April 1987
- journal article
- research article
- Published by Elsevier in Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism
- Vol. 918 (3) , 250-259
- https://doi.org/10.1016/0005-2760(87)90228-1
Abstract
No abstract availableKeywords
This publication has 32 references indexed in Scilit:
- New Tools for the Study of Niemann-Pick Disease: Analogues of Natural Substrate and Epstein-Barr Virus-transformed Lymphoid Cell LinesPediatric Research, 1985
- Biochemical studies in Niemann‐Pick disease. III: In vitro and in vivo assays of sphingomyelin degradation in cultured skin fibroblasts and amniotic fluid cells for the diagnosis of the various forms of the diseaseClinical Genetics, 1985
- Impairment of exogenous sphingomyelin degradation in cultured fibroblasts from familial hypercholesterolemiaFEBS Letters, 1984
- Lysosomal involvement in cellular turnover of plasma membrane sphingomyelinBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1984
- Uptake and metabolism of radioactively labeled sphingomyelin in cultured skin fibroblasts from controls and patients with niemann-pick disease and other lysosomal storage diseasesBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1983
- In situ degradation of sphingomyelin by cultured normal fibroblasts and fibroblasts from patients with Niemann-Pick disease type A and CBiochemical and Biophysical Research Communications, 1982
- Metabolism of sphingomyelin by intact cultured fibroblasts: Differentiation of Niemann-Pick disease types A and BBiochemical and Biophysical Research Communications, 1982
- A fluorometric determination of sphingomyelinase by use of fluorescent derivatives of sphingomyelin, and its application to diagnosis of Niemann-Pick disease.Clinical Chemistry, 1980
- NIEMANN PICK DISEASE: PRESENCE OF THE MAGNESIUM‐DEPENDENT SPHINGOMYELINASE IN BRAIN OF THE INFANTILE FORM OF THE DISEASE1Journal of Neurochemistry, 1978
- Methods for methanolysis of sphingolipids and direct determination of long‐chain bases by gas chromatographyJournal of Oil & Fat Industries, 1965