Congenital hepatic fibrosis, liver cell carcinoma and adult polycystic kidneys

Abstract
In reviewing the literature, we found no liver cell carcinoma (LCC) or well-documented adult polycystic kidneys (APK) associated with congenital hepatic fibrosis (CHF). We report a 69-year-old man with CHF, LCC, APK, duplication cyst of distal portion of stomach, two calcified splenic artery aneurysms, myo-cardial fibrosis and muscular hypertrophy of esophagus. The LCC was grossly pedunculated and microscopically showed prominent fibrosis and hyaline intracytoplasmic inclusions in the tumor cells.

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