HEREDITARY ECTODERMAL DYSPLASIA OF THE ANHIDROTIC TYPE

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Abstract
Cases of hereditary ectodermal dysplasia of the anhidrotic type are still sufficiently rare to warrant publication, and when 2 classic cases in one family are discovered, we feel justified in bringing the subject before dermatologists once more. The question of the designation of this disease—congenital ectodermal defect or hereditary ectodermal dysplasia of the anhidrotic type —is of interest and has not been fully settled. As the title of our paper signifies, we prefer the latter term as being more descriptive of the condition under discussion. Congenital ectodermal defect may apply to a great variety of congenital anomalies of the ectoderm, from minor aberrations in dentition, abnormalities of the nails or hirsute adornment to a major defect presenting all these difficulties, combined with absence of sweat glands and marked decrease in sebaceous gland formation as well. The term congenital ectodermal defect has led to considerable confusion in the literature—so much that

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