Severe mental retardation in a patient with tricho-rhino-phalangeal syndrome type I and 8q deletion

Abstract
We report a 19-year-old boy with an interstitial deletion of the long arm of chromosome 8 (46, XY, del(8)(pter→q23.3∶∶q24.13→qter)). He shows the typical clinical symptoms of tricho-rhino-phalangeal syndrome (TRPI) and severe mental retardation, however without multiple exostoses. This is the second report of a combination of abnormalities and interstitial deletion of 8q.