PSEUDOVASCULAR RING RESULTING FROM RIGHT LUNG AGENESIS, NORMAL AORTIC ARCH, AND PATENT DUCTUS ARTERIOSUS

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Abstract
A case is described with clinical, roentgenographic and anatomic features of pseudovascular ring not previously reported in the literature. Early neonatal proof of a congenitally absent right lung did not explain the infant's respiratory distress, and the suspected tracheal compression could not be verified before her death in the 11th week. Postmortem examination disclosed that shifting of the heart into the right thoracic cavity had caused a patent ductus arteriosus to impinge on the distal trachea. The aortic arch was on the left as is normal. Although mimicking the signs and symptoms of a true vascular ring, this arrangement did not actually encircle the mediastinal structures. It is postulated that awareness of this entity will permit its early diagnosis in some future case, thus initiating a lifesaving ablation of the constricting ductus arteriosus.

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