FETAL HEMOGLOBIN IN POLYCYTHEMIA-VERA - CELLULAR-DISTRIBUTION IN 50 UNSELECTED PATIENTS
- 1 January 1979
- journal article
- research article
- Vol. 53 (6) , 1148-1155
Abstract
Fetal Hb was studied in 50 unselected patients with polycythemia vera with chemical determinations of Hb F and measurements of F-cell [cells synthesizing Hb F] levels using fluorescent anti-Hb F antibodies. Although in the majority of the patients Hb F production did not differ from that in normal controls, in 20% of the patients F-cell values were above the normal range. There was no correlation between F-cell values and duration of disease, treatment modality, presence of myelofibrosis or hematologic parameters at the time of study. In 5 of 50 patients 30-45% of the erythrocytes contained Hb F. Such striking elevations of F cells may reflect a distorted differentiation of erythroid precursor cells in certain patients with this disorder.This publication has 9 references indexed in Scilit:
- HB-F PRODUCTION IN ENDOGENOUS COLONIES OF POLYCYTHEMIA-VERA1979
- Polycythemia vera. The in vitro response of normal and abnormal stem cell lines to erythropoietin.Journal of Clinical Investigation, 1978
- Erythroid Progenitors Circulating in the Blood of Adult Individuals Produce Fetal Hemoglobin in CultureScience, 1978
- Cellular Distribution of Hemoglobin F in a Clonal Hemopoietic Stem-Cell DisorderNew England Journal of Medicine, 1978
- FETAL HEMOGLOBIN IN PAROXYSMAL NOCTURNAL HEMOGLOBINURIA (PNH) - EVIDENCE FOR DERIVATION OF HBF-CONTAINING ERYTHROCYTES (F-CELLS) FROM PNH CLONE AS WELL AS FROM NORMAL HEMATOPOIETIC STEM-CELL LINES1978
- Hemoglobin F synthesis in vitro: evidence for control at the level of primitive erythroid stem cells.Proceedings of the National Academy of Sciences, 1977
- Polycythemia Vera: Stem-Cell and Probable Clonal Origin of the DiseaseNew England Journal of Medicine, 1976
- Identification of Haemoglobin S in Red Cells and Normoblasts, Using Fluorescent Anti-Hb S AntibodiesBritish Journal of Haematology, 1976
- A MODEL FOR THE PERSISTENCE OR REACTIVATION OF FETAL HqMOGLOBIN PRODUCTIONThe Lancet, 1976