The psychological functioning of three children with cerebral gigantism was explored, and similarities in intellectual, behavioral, and educational characteristics were found. The children showed a marked unevenness in their intellectual development, perseverative responding, word-finding problems, psychomotor slowness, and concrete thinking. All had well-developed reading skills but impairments in arithmetic reasoning and computation. The authors raise the possibility that children with cerebral gigantism may be easily misidentified as mentally retarded on routine psychometric evaluation. Also, the educational aspects of this syndrome may be quite complex and of considerable importance in the planning for these children.