Abstract
Two unrelated patients with a de novo partial trisomy 8 (q21.fwdarw.qter) are presented. The children had strikingly similar phenotypes, characterized by a wide face with hypertelorism, a broad based nose, malformed ears, micrognathia and a very short neck. A cleft palate, cardiac defects and hydronephrosis were present in both patients. The relation between the 8qter syndrome and trisomy 8 (Warkany syndrome) is discussed.