Functional abnormalities of heparan sulfate in mucopolysaccharidosis-I are associated with defective biologic activity of FGF-2 on human multipotent progenitor cells
Open Access
- 15 September 2005
- journal article
- Published by American Society of Hematology in Blood
- Vol. 106 (6) , 1956-1964
- https://doi.org/10.1182/blood-2005-02-0657
Abstract
In mucopolysaccharidosis-I (MPS-I), α-L-iduronidase deficiency leads to progressive heparan sulfate (HS) and dermatan sulfate (DS) glycosaminoglycanKeywords
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