Group C Niemann‐Pick disease: faulty regulation of low‐density lipoprotein uptake and cholesterol storage in cultured fibroblasts
- 1 July 1987
- journal article
- research article
- Published by Wiley in The FASEB Journal
- Vol. 1 (1) , 40-45
- https://doi.org/10.1096/fasebj.1.1.3609608
Abstract
Incubation of mutant Niemann-Pick C fibroblasts with low-density lipoprotein (LDL) resulted in excessive internalization of lipoprotein and extensive cellular over-accumulation of unesterified choles...Keywords
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