Up‐Regulation of Protein Chaperones Preserves Viability of Cells Expressing Toxic Cu/Zn‐Superoxide Dismutase Mutants Associated with Amyotrophic Lateral Sclerosis
Open Access
- 1 February 1999
- journal article
- research article
- Published by Wiley in Journal of Neurochemistry
- Vol. 72 (2) , 693-699
- https://doi.org/10.1046/j.1471-4159.1999.0720693.x
Abstract
: Mutations in the Cu/Zn‐superoxidedismutase (SOD‐1) gene underlie some familial cases of amytotrophic lateral sclerosis, a neurodegenerative disorder charactreized by loss of cortical, brai...Keywords
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