Pathogenesis, diagnosis and treatment of Rasmussen encephalitis: A European consensus statement
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Open Access
- 5 January 2005
- journal article
- review article
- Published by Oxford University Press (OUP) in Brain
- Vol. 128 (3) , 454-471
- https://doi.org/10.1093/brain/awh415
Abstract
Rasmussen encephalitis (RE) is a rare but severe immune-mediated brain disorder leading to unilateral hemispheric atrophy, associated progressive neurological dysfunction and intractable seizures. Recent data on the pathogenesis of the disease, its clinical and paraclinical presentation, and therapeutic approaches are summarized. Based on these data, we propose formal diagnostic criteria and a therapeutic pathway for the management of RE patients.Keywords
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