Abstract
Two cases of diffuse interstitial pulmonary fibrosis with arthritis are presented. The response of the pulmonary lesions to steroids is better correlated with the maturity of the fibroblastic process, as seen in the lung biopsy, than with duration of the disease. Rheumatoid disease occurs in about 20% of the recorded cases of diffuse interstitial pulmonary fibrosis. It is suggested that cases of diffuse interstitial pulmonary fibrosis without arthritis be classified as Hamman-Rich syndrome. If arthritis is present, such cases should be classified as rheumatoid lung disease.

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