Skleromyxödem Arndt-Gottron und assoziierte Phänomene
- 1 January 1984
- journal article
- research article
- Published by S. Karger AG in Dermatology
- Vol. 169 (1) , 29-35
- https://doi.org/10.1159/000249563
Abstract
Scleromyxedema is an uncommon fibromucinous connective tissue disease characterized by accumulation of mucinous material in the dermis. A monoclonal paraprotein is regularly identified. A review of the literature (57 cases) shows the exceptional association of scleromyxedema with multiple myeloma (8.7%) and Waldenstrom macroglobulinemia (3.5%). A man with scleromyxedema, IgG lambda paraproteinemia, and sclerodactylia, as a special sign of scleromyxedema, is reported. Melphalan is the drug of choice in serious cases, but not effective in sclerodactylia.This publication has 6 references indexed in Scilit:
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- Treatment of scleromyxedema with melphalanArchives of Dermatology, 1979
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