FAMILIAL PALLIDAL DISEASE WITH UNUSUAL FEATURES IN NEGROES

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Abstract
Many familial extrapyramidal syndromes have been described in the literature. Outstanding are: the pseudosclerosis group, described by Wilson, Vogt's disease and Hallervorden-Spatz' disease. It is known that there is a familial and hereditary element in Wilson's disease. The familial aspect has been studied by Rausch and Schilder,1who observed two sisters with the condition, and recently by Curran,2who observed a family, with consanguinity of the parents, in which all of the five children showed signs of pseudosclerosis. The hereditary aspect has been studied carefully by Kehrer.3 Vogt's disease, also known as status marmoratus, was first described by C. and O. Vogt. This disease is not so well known, and a short description will not be amiss. It is a disease in which there are spastic states and anomalies of posture of extrapyramidal character, with involuntary movementsof choreic and especially of athetoid type. Associated movements, forced laughing