Erdheim-Chester disease: a case report and literature overview
- 26 January 1999
- journal article
- case report
- Published by Springer Nature in European Radiology
- Vol. 9 (1) , 153-158
- https://doi.org/10.1007/s003300050647
Abstract
Erdheim-Chester (EC) disease belongs to the group of lipoid granulomatosis. Symmetric sclerosis of the meta- and diaphysis of long tubular bones are pathognomonic radiologic changes. Additionally, other skeletal segments can be affected. Extraskeletal manifestations can occur in almost all organs; lungs, pericardium, retroperitoneum, skin, and orbita play particularly important roles. The last case of 38 cases of Erdheim-Chester disease with an extraordinary mediastinal and perirenal involvement is described. For the second time following the initial description by Chester, an axial skeletal pattern of eburnated vertebra is shown.Keywords
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