THE FOUR cases reported below were so alike in appearance and course that the patients were undoubtedly suffering from the same disease, a disease which does not seem to have been described previously in dermatological or pediatric literature and which cannot be satisfactorily classified under a known diagnosis. The first two cases have already been reported by me1as dermatitis herpetiformis Duhring. To these cases I can now add that of a younger sister of the patient in Case 1, who exhibited the same syndrome, though not as severely, and another case, presented before the Danish Dermatological Society on March 5, 1952. Case1.—The patient was born in a municipal lying-in department in Odense at term; delivery was normal. The baby was a first-born child. The weight at birth was 3,800 gm. The parents were healthy, and there was no instance of consanguinity in the family. The pregnancy had been normal, but there was profuse bleeding after delivery. The infant