Inhibition of oxidative phosphorylation by palmitoyl-CoA in digitonin permeabilized fibroblasts: implications for long-chain fatty acid β-oxidation disorders
- 15 August 1995
- journal article
- Published by Elsevier in Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
- Vol. 1272 (1) , 14-20
- https://doi.org/10.1016/0925-4439(95)00064-b
Abstract
No abstract availableKeywords
This publication has 38 references indexed in Scilit:
- Medium–chain acyl-coenzyme A dehydrogenase deficiency: Clinical course in 120 affected childrenThe Journal of Pediatrics, 1994
- Fatty acid oxidation disorders: A new class of metabolic diseasesThe Journal of Pediatrics, 1992
- Beta-oxidation of long-chain fatty acids by human fibroblasts: Evidence for a novel long-chain acyl-coenzyme a dehydrogenaseBiochemical and Biophysical Research Communications, 1992
- Clinical diagnosis of long-chain acyl-coenzyme A-dehydrogenase deficiency: Use of stress and fat-loading testsThe Journal of Pediatrics, 1991
- Disorders of mitochondrial β‐oxidation: Prenatal and early postnatal diagnosis and their relevance to Reye's syndrome and sudden infant deathJournal of Inherited Metabolic Disease, 1989
- Primary Carnitine Deficiency Due to a Failure of Carnitine Transport in Kidney, Muscle, and FibroblastsNew England Journal of Medicine, 1988
- Recognition of medium-chain acyl-CoA dehydrogenase deficiency in asymptomatic siblings of children dying of sudden infant death or Reye-like syndromesThe Journal of Pediatrics, 1986
- Fasting hypoglycemia resulting from hepatic carnitine palmitoyl transferase deficiencyThe Journal of Pediatrics, 1981
- Muscle Carnitine Palmityltransferase Deficiency and MyoglobinuriaScience, 1973
- The inhibition of adenine nucleotide translocase activity by oleoyl CoA and its reversal in rat liver mitochondriaBiochemical and Biophysical Research Communications, 1971