Identification of meso-hydroxyuroporphyrin I in the urine of a patient with congenital erythropoietic porphyria
- 15 November 1989
- journal article
- research article
- Published by Portland Press Ltd. in Biochemical Journal
- Vol. 264 (1) , 293-295
- https://doi.org/10.1042/bj2640293
Abstract
A new porphyrin, meso-hydroxyuroporphyrin I, was isolated from the urine of a patient with congenital erythropoietic porphyria. The structure was characterized as the methyl ester, ethyl ester and acetoxy derivatives by fast-atom-bombardment m.s., by conversion into uroporphyrin I and by chemical synthesis.This publication has 6 references indexed in Scilit:
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