Frameshift Codon 5 [FSC-5 (−CT)] Thalassemia; a Novel Mutation Detected in a Greek Patient

Abstract
Sequence analysis and dot-blot hybridization of DNA from a Greek patient with a transfusion dependent thalassemia revealed the combination of a βIVS-I-1 G→-A mutation (β˚-thalassemia) and a hitherto undescribed frameshift mutation; the latter concerns the absence of a CT dinucleotide from codon 5 and results in a termination signal at the new codon 21 (also a β˚-thalassemia).