Homocystinuria: Excretion of a New Sulfur-Containing Amino Acid in Urine
- 6 May 1966
- journal article
- research article
- Published by American Association for the Advancement of Science (AAAS) in Science
- Vol. 152 (3723) , 776-778
- https://doi.org/10.1126/science.152.3723.776
Abstract
An unusual homocysteine-containing compound, 5-amino-4-imidazolecarboxamide-5′- S -homocysteinylriboside, was isolated from the urine of a child with homocystinuria and detected in the urines of six homocystinurics. Its metabolic origin is not clear, and the data suggest the existence in man of now unknown alternate pathways for the metabolism of methionine and of purines.This publication has 13 references indexed in Scilit:
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