Peroxisomal beta-oxidation of branched chain fatty acids in human skin fibroblasts.
Open Access
- 1 November 1992
- journal article
- Published by Elsevier in Journal of Lipid Research
- Vol. 33 (11) , 1597-1605
- https://doi.org/10.1016/s0022-2275(20)41382-3
Abstract
No abstract availableKeywords
This publication has 24 references indexed in Scilit:
- Diagnosis of Refsum's disease using [1-14C]phytanic acid as substrateClinical Genetics, 2008
- Structural and functional features of different types of cytoplasmic fatty acid-binding proteinsBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1991
- Rhizomelic chondrodysplasia punctata. Deficiency of 3-oxoacyl-coenzyme A thiolase in peroxisomes and impaired processing of the enzyme.Journal of Clinical Investigation, 1990
- Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligasesBiochemistry, 1990
- Mitochondrial oxidation of phytanic acid in human and monkey liver: Implication that Refsum's disease is not a peroxisomal disorderBiochemical and Biophysical Research Communications, 1990
- Rhizomelic chondrodysplasia punctata: Clinical, pathologic, and biochemical findings in two patientsThe Journal of Pediatrics, 1988
- Biochemical abnormalities in rhizomelic chondrodysplasia punctataThe Journal of Pediatrics, 1988
- Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.Journal of Clinical Investigation, 1987
- A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye bindingAnalytical Biochemistry, 1976
- Refsum's disease: characterization of the enzyme defect in cell cultureJournal of Clinical Investigation, 1969