A High Skin Protoporphyrin Level in Erythropoietic Protoporphyria
- 1 January 1980
- journal article
- research article
- Published by Tohoku University Medical Press in The Tohoku Journal of Experimental Medicine
- Vol. 130 (1) , 97-100
- https://doi.org/10.1620/tjem.130.97
Abstract
A high skin protoporphyrin level (4.36 μ/g wet weight) was detected in a 14-year-old girl with erythropoietic protoporphyria who died of protoporphyrin hepatopathy cirrhosis. Excess protoporphyrin was detected in the skin by our assay technique which was assumed to cause severe skin photosensitivity.Keywords
This publication has 1 reference indexed in Scilit:
- Erythropoietic protoporphyria: Juvenile protoporphyrin hepatopathy cirrhosis and deathThe Journal of Pediatrics, 1977