Diastematomyelia

Abstract
Diastematomyelia is a congenital malformation of the neural axis characterized by a sagittal division of a segment of the spinal cord or cauda equina and usually associated with anomalous development of the vertebrae. The two lateral portions of the cord are separated by an osseous or fibrocartilaginous septum which is attached anteriorly to one or more vertebral bodies, posteriorly to the dura, and occasionally to the deformed vertebral arches as well. Herren and Edwards (3) were able to collect from the literature 42 cases which they considered examples of true diplomyelia and added another. Since then we have found 9 additional reported cases (1, 2, 5–9). In 1946, Maxwell and Bucy (8) stated that only 4 of the recorded cases were diagnosed before autopsy; these were recognized at operation. No reports have been found of cases in which the diagnosis was made preoperatively. We believe that the diagnosis can be made in most cases by roentgenograms of the spine because of the associated bony abnormalities...
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