Auditory Brain-Stem Responses in Adrenomyeloneuropathy
- 1 September 1983
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Neurology
- Vol. 40 (9) , 574-576
- https://doi.org/10.1001/archneur.1983.04050080074015
Abstract
• We studied three patients with adrenomyeloneuropathy. Complete audiologic assessment was obtained: two patients showed unimpaired peripheral hearing and one showed a mild high-frequency hearing loss. Auditory brain-stem responses were abnormal in both ears of all subjects, with one subject showing no response above wave I, and the other two having significant wave I to III and wave III to V interval prolongations. We concluded that auditory brain-stem response testing provides a simple, valid, reliable method for demonstrating neurologic abnormality in adrenomyeloneuropathy even prior to evidence of clinical signs.This publication has 8 references indexed in Scilit:
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