Neurogenic scapuloperoneal syndrome in childhood.
- 1 October 1980
- journal article
- research article
- Published by BMJ in Journal of Neurology, Neurosurgery & Psychiatry
- Vol. 43 (10) , 888-896
- https://doi.org/10.1136/jnnp.43.10.888
Abstract
Two brothers presented with a slowly progressive scapuloperoneal syndrome starting in early childhood. Initially there were myopathic EMG [electromyogram] changes, but these changed to those of denervation. Neuromuscular biopsies at an interval of 5 yr confirmed the neurogenic character of the muscle atrophy.This publication has 38 references indexed in Scilit:
- Congenital fibre type disproportion myopathy. A histological diagnosis with an uncertain clinical outlook.Archives of Disease in Childhood, 1979
- Scapulo-Peroneal Muscular AtrophyEuropean Neurology, 1976
- Scapuloperoneal atrophy with sensory involvement: Davidenkow's syndrome.Journal of Neurology, Neurosurgery & Psychiatry, 1975
- Adult onset scapuloperoneal myopathy.Journal of Neurology, Neurosurgery & Psychiatry, 1975
- Myogenic Scapuloperoneal Syndrome – Muscular Dystrophy in the K. KindredEuropean Neurology, 1975
- Data on the distribution of fibre types in thirty-six human muscles: An autopsy studyPublished by Elsevier ,1973
- A Case of Scapulo-Tibio-Peroneal SyndromeEuropean Neurology, 1973
- The Neurogenic Scapulo-Peroneal SyndromeEuropean Neurology, 1968
- Unusual type of benign x-linked muscular dystrophy.Journal of Neurology, Neurosurgery & Psychiatry, 1966
- SCAPULOPERONEAL MUSCULAR ATROPHYBrain, 1965