PKU is a reversible neurodegenerative process within the nigrostriatum that begins as early as 4 weeks of age in Pahenu2 mice
- 15 November 2006
- journal article
- Published by Elsevier in Brain Research
- Vol. 1127 (1) , 136-150
- https://doi.org/10.1016/j.brainres.2006.09.101
Abstract
No abstract availableKeywords
This publication has 40 references indexed in Scilit:
- Oxidative stress in patients with phenylketonuriaBiochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 2005
- Neuroprotective effect of dextromethorphan in the MPTP Parkinson's disease model: role of NADPH oxidaseThe FASEB Journal, 2004
- Plasma thiols and their determinants in phenylketonuriaEuropean Journal of Clinical Nutrition, 2003
- Stable therapeutic serum levels of human alpha-1 antitrypsin (AAT) after portal vein injection of recombinant adeno-associated virus (rAAV) vectorsGene Therapy, 2001
- Role of Free Radicals in the Neurodegenerative DiseasesDrugs & Aging, 2001
- Context Dependence of Different Modules for Posttranscriptional Enhancement of Gene Expression from Retroviral VectorsMolecular Therapy, 2000
- Influence of promoter and WHV post-transcriptional regulatory element on AAV-mediated transgene expression in the rat brainGene Therapy, 2000
- Characterization of Mutations at the Mouse Phenylalanine Hydroxylase LocusGenomics, 1997
- A study of cerebellar and cerebral cortical degeneration in Miniature Poodle pups with emphasis on the ultrastructure of Purkinje cell changesActa Neuropathologica, 1988
- NATURAL HISTORY OF PHENYLKETONURIA AND INFLUENCE OF EARLY TREATMENTThe Lancet, 1974