Polarographic studies of saponin-skinned muscle fibres in patients with mitochondrial myopathies
- 1 January 1994
- journal article
- research article
- Published by Springer Nature in Journal of Inherited Metabolic Disease
- Vol. 17 (3) , 307-310
- https://doi.org/10.1007/bf00711815
Abstract
No abstract availableKeywords
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- Combined deficiencies of the pyruvate dehydrogenase complex and enzymes of the respiratory chain in mitochondrial myopathiesEuropean Journal of Pediatrics, 1992
- Mitochondrial respiratory parameters in cardiac tissue: A novel method of assessment by using saponin-skinned fibersBiochimica et Biophysica Acta (BBA) - Bioenergetics, 1987
- Pyruvate oxidation in rat and human skeletal muscle mitochondriaBiochemical Medicine, 1978