Familial Benign Chronic Pemphigus (Hailey-Hailey) in Negroes

Abstract
In 1939, Hailey and Hailey reported four cases of what they believed to be a new entity, naming it familial benign chronic pemphigus.1 It was described as a vesiculobullous, chronic, benign, recurrent familial disease characteristically involving the sides and nape of the neck, axillae, and inframammary and inguinal creases. Microscopically, suprabasal lacunae and bullae were found. Previously, a number of authors had described cases diagnosed as Darier's disease with prominent moisture and maceration, which resembled this condition. Bukovsky,2 Louste and Barbier,3 and Pels and Goodman,4 among others, described frank vesicles and bullae in Darier's disease. Gougerot and Allée,5 in 1933, reported cases of four blood relatives with a familial hereditary benign bullous disease. Under a variety of titles, many patients demonstrating the criteria enumerated by Hailey and Hailey have been recorded in the literature or reported in society trans

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