Thrombosis of the Inferior Vena Cava and Hepatic Veins (Budd-Chiari Syndrome)

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Abstract
Well-documented cases of hepatic vein occlusion of prolonged duration are extremely rare. In his thorough review of the Budd-Chiari syndrome, Parker (1) could evaluate the chronicity of 133 reported cases of the disease, and of these only 19 had signs or symptoms of hepatic vein occlusion for over 2 years before death and only 10 for over 3 years. The patient in the case reported here survived for 13 years or more after clinical signs suggesting inferior vena caval obstruction and for more than 4 years after evidence of essentially total hepatic venous obstruction. The case is thought to represent