Metabolism of malonic semialdehyde in man
- 15 October 1983
- journal article
- research article
- Published by Portland Press Ltd. in Biochemical Journal
- Vol. 216 (1) , 81-85
- https://doi.org/10.1042/bj2160081
Abstract
Malonic semialdehyde is formed in the alternative pathway of propionate metabolism and in the catabolism of beta-alanine. Studies of these pathways in cultured cells from a patient with mitochondrial malonyl-CoA decarboxylase deficiency indicate that malonic semialdehyde is directly converted into acetyl-CoA in man.This publication has 16 references indexed in Scilit:
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