Idiopathic extrahepatic biliary atresia: Recurrence in sibs in two families
- 1 October 1988
- journal article
- research article
- Published by Wiley in American Journal of Medical Genetics
- Vol. 31 (2) , 421-426
- https://doi.org/10.1002/ajmg.1320310222
Abstract
Since 1855, 11 instances of familial extrahepatic biliary atresia (EHBA) have been described. Genetic, environmental, vascular, and infectious causes for this disorder have been proposed. We report on 2 families each with 2 sibs with EHBA. We suggest that a genetic susceptibility to an environmental insult to the biliary tree may be responsible for the genesis of this disease.Keywords
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