Long‐term complications in Hunter's syndrome
- 1 August 1979
- journal article
- Published by Wiley in Clinical Genetics
- Vol. 16 (2) , 125-132
- https://doi.org/10.1111/j.1399-0004.1979.tb00861.x
Abstract
This report describes the clinical and investigative findings in a 31‐year‐old man with Hunter's syndrome, showing evidence of severe multisystem involvement. Papilloedema has been present for at least 8 years with no evidence of progressive visual impairment. His most serious and life‐threatening complications are laryngeal oedema and tracheal narrowing, which both compromise his respiratory function and constitute a major anaesthetic risk.Keywords
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