Update in Cystic Fibrosis 2005
- 1 May 2006
- journal article
- review article
- Published by American Thoracic Society in American Journal of Respiratory and Critical Care Medicine
- Vol. 173 (9) , 944-947
- https://doi.org/10.1164/rccm.2601006
Abstract
No abstract availableThis publication has 43 references indexed in Scilit:
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- Embryonic Stem Cells Generate Airway Epithelial TissueAmerican Journal of Respiratory Cell and Molecular Biology, 2005
- Pancreatic enzyme therapy and clinical outcomes in patients with cystic fibrosisThe Journal of Pediatrics, 2005
- Impact of the ΔF508 Mutation in First Nucleotide-binding Domain of Human Cystic Fibrosis Transmembrane Conductance Regulator on Domain Folding and StructureJournal of Biological Chemistry, 2005
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- The ΔF508 cystic fibrosis mutation impairs domain-domain interactions and arrests post-translational folding of CFTRNature Structural & Molecular Biology, 2004
- Adult stem cells from bone marrow stroma differentiate into airway epithelial cells: Potential therapy for cystic fibrosisProceedings of the National Academy of Sciences, 2004