L-Carnitine Insufficiency in Disorders of Organic acid Metabolism: Response to L-Carnitine by Patients with Methylmalonic Aciduria and 3-Hydroxy-3-methylglutaric Aciduria

This publication has 7 references indexed in Scilit:

• Application of high resolution fast atom bombardment and constant B/E ratio linked scanning to the identification and analysis of acylcarnitines in metabolic disease
  Journal of Mass Spectrometry, 1984
• Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl-CoA/CoA ratios by l-carnitine in vivo
  Biochemical Society Transactions, 1983
• Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups.
  Archives of Disease in Childhood, 1983
• C6—C10-Dicarboxylic Aciduria: Investigations of a Patient with Riboflavin Responsive Multiple Acyl-CoA Dehydrogenation Defects
  Pediatric Research, 1982
• L-CARNITINE THERAPY IN PROPIONICACIDAEMIA
  The Lancet, 1982
• Organic Acids in Man
  Published by Springer Nature ,1982
• Carnitine metabolism in the fasting rat.
  Journal of Biological Chemistry, 1978