First Case of Acquired Functional CI INH Deficiency: Association with Angioedema during Churg and Strauss Vasculitis
- 1 January 1984
- journal article
- case report
- Published by S. Karger AG in International Archives of Allergy and Immunology
- Vol. 74 (3) , 284-285
- https://doi.org/10.1159/000233560
Abstract
This report deals with the first case of acquired functional CI INH deficiency with normal anti-genic CI INH level which was detected in a young girl with angioedema and Churg and Strauss vasculitis. This complement abnormality was associated with slightly depressed levels of CH50, C4 and C2, but a normal level of C3, and high levels of total IgE and IgM rheumatoid factors. Finally, most of these abnormalities dis-apeared after corticosteroid therapy and clinical improvement.Keywords
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