Uptake and stability of human and bovine acid α-glucosidase in cultured fibroblasts and skeletal muscle cells from glycogenosis type II patients

This publication has 31 references indexed in Scilit:

• Isolation and characterization of a precursor form of lysosomal α‐glucosidase from human urine
  European Journal of Biochemistry, 1984
• Adult forms of glycogenosis type II
  FEBS Letters, 1982
• Enhanced proteolytic degradation of normal β-galactosidase in the lysosomal storage disease with combined β-galactosidase and neuraminidase deficiency
  Biochimica et Biophysica Acta (BBA) - Protein Structure and Molecular Enzymology, 1982
• Deficiency of UDP-N-acetylglucosamine: Lysosomal enzyme N-acetylglucosamine-1-phosphotransferase in organs of I-cell patients
  Biochemical and Biophysical Research Communications, 1982
• Is there a mechanism for introducing acid hydrolases into liver lysosomes that is independent of mannose 6-phosphate recognition? evidence from I-cell disease
  Biochemical and Biophysical Research Communications, 1982
• Transport and processing of lysosomal enzymes by smooth muscle cells and endothelial cells
  Experimental Cell Research, 1981
• Specific changes in cellular glycoproteins and surface proteins during myogenesis in clonal muscle cells
  Developmental Biology, 1981
• Phenotypic expression in cybrids derived from teratocarcinoma cells fused with myoblast cytoplasms
  Experimental Cell Research, 1979
• Recognition and receptor-mediated uptake of a lysosomal enzyme, α-l-iduronidase, by cultured human fibroblasts
  Cell, 1977
• Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4
  Nature, 1970